IRIS Institutional Research Information System - OPENBS Open Archive UniBS

FRA, ANNAMARIA
 Distribuzione geografica
Salva come PNG Salva come JPEG
Continente #
NA - Nord America 3.166
EU - Europa 1.928
AS - Asia 1.027
SA - Sud America 9
OC - Oceania 6
AF - Africa 5
Continente sconosciuto - Info sul continente non disponibili 5
Totale 6.146
Salva come PNG Salva come JPEG
Nazione #
US - Stati Uniti d'America 3.154
PL - Polonia 612
CN - Cina 435
UA - Ucraina 309
IT - Italia 298
SG - Singapore 259
GB - Regno Unito 189
DE - Germania 177
HK - Hong Kong 163
FI - Finlandia 105
TR - Turchia 74
RU - Federazione Russa 73
IE - Irlanda 63
VN - Vietnam 35
IN - India 33
BE - Belgio 23
FR - Francia 20
SE - Svezia 17
CH - Svizzera 13
CA - Canada 9
ID - Indonesia 9
NL - Olanda 7
AU - Australia 6
ES - Italia 5
EU - Europa 5
JP - Giappone 5
AR - Argentina 4
AT - Austria 4
CZ - Repubblica Ceca 4
AZ - Azerbaigian 3
BR - Brasile 3
IL - Israele 3
MU - Mauritius 3
PH - Filippine 3
PT - Portogallo 3
RO - Romania 3
CL - Cile 2
MX - Messico 2
AE - Emirati Arabi Uniti 1
DK - Danimarca 1
EG - Egitto 1
HR - Croazia 1
JM - Giamaica 1
JO - Giordania 1
KG - Kirghizistan 1
KR - Corea 1
LK - Sri Lanka 1
LT - Lituania 1
ZA - Sudafrica 1
Totale 6.146
Salva come PNG Salva come JPEG
Città #
Warsaw 612
Fairfield 452
Woodbridge 289
Ashburn 247
Jacksonville 235
Chandler 217
Wilmington 193
Ann Arbor 192
Cambridge 190
Houston 189
Singapore 189
Seattle 184
Hong Kong 160
Princeton 112
Lancaster 100
Brescia 96
Beijing 90
Nanjing 74
Dearborn 67
Dublin 63
Helsinki 63
Istanbul 57
New York 55
San Diego 33
Nanchang 29
Rome 29
Dong Ket 28
Shanghai 28
Moscow 25
Jiaxing 23
Milan 23
Brussels 22
Changsha 22
Shenyang 21
Tianjin 21
Des Moines 18
Hebei 18
London 16
Jinan 15
Kocaeli 14
Los Angeles 12
Hangzhou 11
Kunming 10
Lugano 10
Phoenix 10
Zhengzhou 10
Guangzhou 9
Jakarta 9
Pune 9
Saratoga Springs 9
Verona 8
Lanzhou 7
Lappeenranta 7
Orange 7
Taizhou 7
Boardman 6
Frankfurt am Main 6
Ho Chi Minh City 6
Ningbo 6
San Francisco 6
Villongo 6
Monza 5
Nuremberg 5
Rhinelander 5
Brno 4
Buenos Aires 4
Changchun 4
Hefei 4
Ilford 4
Indiana 4
Kilburn 4
Toronto 4
Trieste 4
Vienna 4
Baku 3
Borgosatollo 3
Boston 3
Bucha 3
Council Bluffs 3
Falkenstein 3
Haikou 3
Miami 3
Minocqua 3
Norwalk 3
Oxford 3
Salò 3
Tel Aviv 3
Aparecida de Goiânia 2
Barcelona 2
Bergamo 2
Brooklyn 2
Castiglione Chiavarese 2
Chicago 2
Cremona 2
East Brunswick 2
Ferrara 2
Guidonia 2
Hounslow 2
Leicester 2
Lonato 2
Totale 4.802
Salva come PNG Salva come JPEG
Nome #
The pathological Trento variant of alpha-1-antitrypsin (E75V) shows non-classical behaviour during polymerization 254
Cysteines as Redox Molecular Switches and Targets of Disease 228
Intermittent C1-Inhibitor Deficiency Associated with Recessive Inheritance: Functional and Structural Insight 219
Characterisation of a type II functionally-deficient variant of alpha-1-antitrypsin discovered in the general population 192
Stability and structural change in the pathological polymerisation of alpha 1-antitrypsin 174
Quality control of ER synthesized proteins: an exposed thiol group as a three-way switch mediating assembly, retention and degradation 166
Developmental regulation of IgM secretion: the role of the carboxy-terminal cysteine 163
Different molecular behavior of CD40 mutants causing hyper-IgM syndrome. 162
Identification and characterisation of eight novel SERPINA1 null mutations. 159
Caveolin-1 and -2 in the exocytic pathway of MDCK cells 138
Real-world clinical applicability of pathogenicity predictors assessed on SERPINA1 mutations in alpha-1-antitrypsin deficiency 133
Exposed thiols confer localization in the endoplasmic reticulum by retention rather than retrieval 127
A photo-reactive derivative of ganglioside GM1 specifically cross-links VIP21-caveolin on the cell surface 126
The Decrease of Mineralcorticoid Receptor Drives Angiogenic Pathways in Colorectal Cancer 126
Cutting edge: scavenging of inflammatory CC chemokines by the promiscuous putatively silent chemokine receptor D6 123
Aberrant disulphide bonding contributes to the ER retention of alpha1-antitrypsin deficiency variants 121
Cellular models for the serpinopathies 120
De novo formation of caveolae in lymphocytes by expression of VIP21-caveolin 117
Differential recognition and scavenging of native and truncated macrophage-derived chemokine (macrophage-derived chemokine/CC chemokine ligand 22) by the D6 decoy receptor 115
Degradation of unassembled soluble Ig subunits by cytosolic proteasomes: evidence that retrotranslocation and degradation are coupled events 115
The efficiency of cysteine-mediated intracellular retention determines the differential fate of secretory IgA and IgM in B and plasma cells 111
Phenotypic behavior of C2C12 myoblasts upon expression of the dystrophy-related caveolin-3 P104L and TFT mutants 111
Three new alpha1-antitrypsin deficiency variants help to define a C-terminal region regulating conformational change and polymerization. 110
CHOP-independent apoptosis and pathway-selective induction of the UPR in developing plasma cells 109
Characterization of a mouse endothelium lymphatic cell line. 109
Molecular characterization of the new defective P(brescia) alpha1-antitrypsin allele. 108
Generation and characterization of a mouse lymphatic endothelial cell line 106
Alpha1-antitrypsin deficiency: a twenty-five years' experience. 105
Mechanisms of interleukin-6 protection against ischemia-reperfusion injury in rat liver 101
Genomic organization and transcriptional analysis of the human genes coding for caveolin-1 and caveolin-2 100
The endoplasmic reticulum as a site of protein degradation 100
Intrahepatic heteropolymerization of M and Z alpha-1-antitrypsin 99
Human caveolin-1 and caveolin-2 are closely linked genes colocalized with WI-5336 in a region of 7q31 frequently deleted in tumors 96
Progressively impaired proteasomal capacity during terminal plasma cell differentiation 96
Functional characterization of amino acid variants of the reactive-center-loop of alpha-1-antitrypsin 95
Detergent-insoluble glycolipid microdomains in lymphocytes in the absence of caveolae 91
Patogenesi delle malattie da alterato trasporto e accumulo proteico nella via secretoria 91
A case of remittent C1-inhibitor deficiency 90
Fab fragment of an antibody selective for wild-type alpha-1-antitrypsin in complex with its antigen 86
Different mechanisms cause ER retention of rare alpha1-antitrypsin deficiency variants 84
Aberrant disulphide interactions contribute to the secretory deficiency of Alpha 1-Antitrypsin mutants 83
Assembly and secretion of antibodies during B cell development 78
Modulating secretion of antibodies 78
Molecular characterization of new variants associated with alpha-1-antitrypsin deficiency (AATD) 78
Heteropolymerization of α-1-antitrypsin mutants in cell models mimicking heterozygosity 74
Polymers of Z α1-antitrypsin are secreted in cell models of disease 73
Regolazione dei geni coinvolti nella patogenesi dell'angioedema ereditario da carenza di C1 inibitore 71
Fab fragment of an antibody selective for wild-type alpha-1-antitrypsin 71
HIGM3 patients: understanding the mutation effect to develop a therapeutic approach 70
Development of a novel assay to measure alpha-1-antitrypsin inhibitory activity toward neutrophil elastase 67
The molecular species responsible for α1 -antitrypsin deficiency are suppressed by a small molecule chaperone 60
Identification and characterisation of seven novel SERPINA1 null mutations 59
Structural characterisation of tissue-derived, disease-associated polymers of alpha-1-antitrypsin using conformation-selective antibodies and single-particle reconstructions from electron microscopy images 54
Quantification of circulating alpha-1-antitrypsin polymers in dried blood spots 51
Characterization of alpha-1 antitrypsin mutants with an alternative polymerisation mechanism 46
Comprehensive Clinical Diagnostic Pipelines Reveal New Variants in Alpha-1 Antitrypsin Deficiency 41
Human iPSC-Derived 3D Hepatic Organoids in a Miniaturized Dynamic Culture System 36
Identification and characterisation of twenty-two novel SERPINA1 pathological mutations 33
The importance of N186 in the alpha-1-antitrypsin shutter region is revealed by the novel bologna deficiency variant 33
Computational prediction of (alpha-1antitrypsin)-elastase Michaelis complex reveals an exosite contributing to high-affinity interaction 27
Probing of the reactive center loop region of alpha-1-antitrypsin by mutagenesis predicts new type-2 dysfunctional variants 26
Clinical and molecular characterisation of new variants associated to alpha-1-antitrypsin deficiency 26
Neuroserpin: structure, function, physiology and pathology 26
Characterization of Novel Alpha-1-Antitrypsin Coding Variants in a Mammalian Cellular Model 25
Quantification of circulating alpha-1-antitrypsin polymers associated with different SERPINA1 genotypes 18
Identification of an exosite at the neutrophil elastase/alpha‐1‐antitrypsin interface 7
Totale 6.387
Salva come PNG Salva come JPEG
Categoria #
all - tutte 30.359
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 30.359
Salva come PNG Salva come JPEG


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2019/2020426 0 0 0 0 0 0 0 0 107 179 63 77
2020/20211.070 37 95 32 129 56 123 74 113 126 131 83 71
2021/2022530 38 94 14 16 6 28 43 37 21 98 35 100
2022/2023561 73 21 26 43 50 125 2 63 85 12 21 40
2023/2024521 39 14 41 43 26 102 20 27 114 15 11 69
2024/2025773 18 13 14 151 175 124 145 45 88 0 0 0
Totale 6.387